Al Akhfash Ali A, Al Mutairi Mansour B, Al Habshan Fahad M
Cardiac Sciences Department, Paediatric Cardiology, King Abdulaziz Cardiac Centre, National Guard Health Affairs, Riyadh, Saudi Arabia.
J Saudi Heart Assoc. 2009 Oct;21(4):245-8. doi: 10.1016/j.jsha.2009.10.003.
Persistent fifth aortic arch is a rare congenital anomaly that can be discovered incidentally or at postmortem exam. It can be associated with major congenital heart malformations involving the systemic or the pulmonary circuits. It usually has no clinical significance but can be either, beneficial as in systemic outflow tract obstructions or cause hemodynamic compromise when associated with a significant left to right shunt. We report an infant with persistent fifth aortic arch associated with Shone's complex diagnosed accurately by transthoracic echocardiography and confirmed by cardiac catheterization and computed tomography.
永存第五主动脉弓是一种罕见的先天性异常,可在偶然情况下或尸检时发现。它可能与涉及体循环或肺循环的主要先天性心脏畸形相关。它通常无临床意义,但在体循环流出道梗阻时可能有益,而与显著的左向右分流相关时则可能导致血流动力学损害。我们报告一例患有永存第五主动脉弓并伴有肖恩综合征的婴儿,通过经胸超声心动图准确诊断,并经心导管检查和计算机断层扫描证实。