Macedo Robson, Prakasa Kalpana, Tichnell Crystal, Marcus Frank, Calkins Hugh, Lima João A C, Bluemke David A
Russell H. Morgan Department of Radiology and Radiological Science, Johns Hopkins University School of Medicine, MRI Bldg., Rm. 143, 600 N Wolf St., Baltimore, MD 21287, USA.
AJR Am J Roentgenol. 2007 May;188(5):W423-7. doi: 10.2214/AJR.06.0161.
The purpose of this study was to describe the structure and function of the heart in the presence of marked lipomatous infiltration of the right ventricular wall in 13 patients referred for second opinions about fatty infiltration of the right ventricular wall and suspected arrhythmogenic right ventricular dysplasia.
Lipomatous infiltration with right ventricular thickness > or = 6 mm on MRI but without regional or global functional abnormalities of the right ventricle appears to be distinct from fatty right ventricle associated with arrhythmogenic right ventricular dysplasia. The finding of right ventricular fat must be interpreted cautiously to avoid the pharmacologic and defibrillator intervention associated with management of arrhythmogenic right ventricular dysplasia.
本研究旨在描述13例因右心室壁脂肪浸润及疑似致心律失常性右心室发育不良而寻求二次诊断的患者,其右心室壁存在明显脂肪浸润时心脏的结构和功能。
MRI显示右心室厚度≥6mm的脂肪浸润,但无右心室局部或整体功能异常,这似乎与致心律失常性右心室发育不良相关的脂肪性右心室不同。必须谨慎解读右心室脂肪的发现,以避免与致心律失常性右心室发育不良管理相关的药物和除颤器干预。