Roul G, Germain P, Coulbois P M, Bareiss P, Dietemann J L
Service de Cardiologie, Hôpital de Hautepierre, avenue Molière, Strasbourg.
J Radiol. 1998 Jun;79(6):541-7.
The diagnosis of localized arrhythmogenic right ventricular dysplasia may be difficult to ascertain. Aside from electrophysiological arguments, visualization of an abnormal right ventricular contraction pattern is of crucial importance for diagnosis. Cine-MR is almost the only examination method which offers detailed informations on the right ventricular contraction pattern. Nine observations of segmental right ventricular contraction abnormalities assessed by cine-MR are described here: dyskinesia of the distal part of the anterior wall (2), of the inferior wall (2), of the right ventricular outflow tract (2); akinesia of the outflow tract (2) and of the inferior wall (1). Morphological abnormalities of the right ventricle are always associated with contraction abnormalities but seem to be less disease specific. Patients should be more readily referred for a cine-MR examination when the diagnosis of localized right ventricular dysplasia is suspected. Cine-MR sequences related to these observations may be reached via Internet at:http:@alsace.u-strasbg.fr/cardio/coeur.htm.
局限性致心律失常性右室发育不良的诊断可能难以确定。除了电生理依据外，观察到异常的右室收缩模式对诊断至关重要。电影磁共振成像（Cine-MR）几乎是唯一能提供有关右室收缩模式详细信息的检查方法。本文描述了通过Cine-MR评估的9例节段性右室收缩异常观察结果：前壁远端运动障碍（2例）、下壁运动障碍（2例）、右室流出道运动障碍（2例）；流出道运动减弱（2例）和下壁运动减弱（1例）。右室形态学异常总是与收缩异常相关，但疾病特异性似乎较低。当怀疑局限性右室发育不良的诊断时，应更容易将患者转诊进行Cine-MR检查。与这些观察结果相关的Cine-MR序列可通过互联网访问：http:@alsace.u-strasbg.fr/cardio/coeur.htm 。
