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一名患有HELLP综合征的患者出现类Purtscher视网膜病变。

Purtscher-like retinopathy in a patient with HELLP syndrome.

作者信息

Stewart Michael W, Brazis Paul W, Guier Christian P, Thota Sindhu H, Wilson Shirley D

机构信息

Department of Ophthalmology, Mayo Clinic College of Medicine, Jacksonville, Florida 32224, USA.

出版信息

Am J Ophthalmol. 2007 May;143(5):886-7. doi: 10.1016/j.ajo.2006.12.005.

Abstract

PURPOSE

To report the antepartum presentation of Purtscher-like retinopathy and hemolysis, elevated liver enzymes, low platelets (HELLP) syndrome that resulted in severe permanent visual loss.

DESIGN

Interventional case report.

METHODS

A 25-year-old primigravida patient at 38.5 weeks gestation presented with severe bilateral loss of vision. Immediate hospitalization with complete evaluation, urgent medical treatment, and cesarean section was performed.

RESULTS

Ophthalmoscopic evaluation showed bilateral Purtscher-like retinopathy. Laboratory studies revealed elevated liver enzymes, thrombocytopenia, and evidence of intravascular coagulation consistent with HELLP syndrome. Despite the successful delivery of a healthy baby, the patient developed permanent visual loss.

CONCLUSION

Purtscher-like retinopathy with permanent visual loss can occur antepartum in patients with HELLP syndrome.

摘要

目的

报告产前出现的类似普尔夏视网膜病变以及溶血、肝酶升高、血小板减少(HELLP)综合征导致严重永久性视力丧失的病例。

设计

介入性病例报告。

方法

一名孕38.5周的25岁初产妇出现严重双侧视力丧失。立即住院进行全面评估、紧急治疗并实施剖宫产。

结果

眼底镜检查显示双侧类似普尔夏视网膜病变。实验室检查显示肝酶升高、血小板减少以及与HELLP综合征相符的血管内凝血迹象。尽管成功分娩出一名健康婴儿,但患者仍出现永久性视力丧失。

结论

HELLP综合征患者产前可出现伴有永久性视力丧失的类似普尔夏视网膜病变。

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