Redondo P
Departamento de Dermatología, Clínica Universitaria de Navarra, Pamplona, España.
Actas Dermosifiliogr. 2007 Apr;98(3):141-58.
Vascular malformations are anomalies always present at birth that, contrary to hemangiomas, never regress and may grow during lifetime. Clinical presentation of vascular malformations is extremely variable and ranges from asymptomatic spots of mere aesthetic concern to lesions with high blood flow or located in critical sites that may be life-threatening. Given the low incidence of these disorders it is difficult to establish therapeutic guidelines. In addition to a correct classification of vascular anomalies, it is necessary a multidisciplinary approach for the follow-up and management of these patients. The first part of this review focuses on the different classifications of vascular anomalies, maintaining as reference the one proposed by the International Society for the Study of Vascular Anomalies (ISSVA). Additionally, clinical features of the different subtypes of vascular anomalies as well as their association in certain syndromes are reviewed.
血管畸形是出生时就存在的异常情况，与血管瘤不同，它们从不消退，且可能在一生中生长。血管畸形的临床表现极为多样，从仅出于美观考虑的无症状斑点到高血流量或位于可能危及生命的关键部位的病变不等。鉴于这些疾病的发病率较低，很难制定治疗指南。除了对血管异常进行正确分类外，对这些患者进行随访和管理还需要多学科方法。本综述的第一部分重点关注血管异常的不同分类，并以国际血管异常研究学会（ISSVA）提出的分类为参考。此外，还综述了血管异常不同亚型的临床特征及其在某些综合征中的关联。
