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头皮松垂症:三例病因不同的病例展示分类系统

Cutis verticis gyrata: three cases with different aetiologies that demonstrate the classification system.

作者信息

Larsen Fiona, Birchall Nicholas

机构信息

Auckland City Hospital, Auckland, New Zealand.

出版信息

Australas J Dermatol. 2007 May;48(2):91-4. doi: 10.1111/j.1440-0960.2007.00343.x.

DOI:10.1111/j.1440-0960.2007.00343.x
PMID:17535195
Abstract

Cutis verticis gyrata describes a scalp condition where there are convoluted folds and deep furrows that resemble the surface of the cerebral cortex. We report three cases of cutis verticis gyrata that demonstrate the current classification structure. The first case is the most commonly described primary non-essential acquired form, appearing in the scalp of an 11-year-old girl with mental retardation. The second case is the primary non-essential congenital form, presenting at birth in a baby with Noonan's syndrome. An association between cutis verticis gyrata and Noonan's syndrome has been rarely described. The third case illustrates secondary cutis verticis gyrata, occurring in a 27-year-old man with discoid eczema.

摘要

回状头皮描述的是一种头皮状况,其特征为存在类似大脑皮质表面的回旋褶皱和深沟。我们报告三例回状头皮病例,以展示当前的分类结构。第一例是最常描述的原发性非必需性后天型,出现在一名患有智力障碍的11岁女孩的头皮上。第二例是原发性非必需性先天性型,在一名患有努南综合征的婴儿出生时即出现。回状头皮与努南综合征之间的关联鲜有描述。第三例说明了继发性回状头皮,发生在一名患有盘状湿疹的27岁男性身上。

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Cutis verticis gyrata: three cases with different aetiologies that demonstrate the classification system.头皮松垂症:三例病因不同的病例展示分类系统
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