Cribier B, Lipsker D, Mutter D, Grosshans E
Clinique Dermatologique, Hôpitaux Universitaires de Strasbourg.
Ann Dermatol Venereol. 1993;120(8):542-5.
Cutis verticis gyrata (CVG) is a rare cause of acquired scalp thickening; in its primary form, the disease does not show any bone involvement. A 19-year old man had noticed a moderate thickening of the scalp at the age of 15. He progressively developed ridges and furrows in the occipital and parietal areas: after a four-year period, there were ten sagittal and irregularly parallel folds. There was neither pain nor pruritus, and the hair had a normal appearance. Complete neurological examination was unremarkable and the patient was of normal intelligence. All biological investigations, including STH and TSH levels, were normal. X-ray examination and tomodensitometry did not show any bone involvement. Our patient was treated by surgical reduction of the scalp areas involved under general anesthesia, with a very good result. This is a typical case of primary CVG. Differential diagnosis of primary cutis verticis gyrata comprises pachydermoperiostosis, cerebriform intradermal nevus and many secondary conditions associated with hypertrophy and folding of the scalp. A relatively simple surgical treatment results in a major reduction of the scalp thickening, and avoids maceration.
头皮回旋状鱼鳞病（CVG）是后天性头皮增厚的罕见病因；在其原发性形式中，该疾病不显示任何骨骼受累情况。一名19岁男性在15岁时注意到头皮有中度增厚。他在枕部和顶叶区域逐渐出现隆起和沟纹：四年后，出现了十条矢状且不规则平行的褶皱。既无疼痛也无瘙痒，头发外观正常。全面的神经系统检查无异常，患者智力正常。所有生物学检查，包括生长激素和促甲状腺激素水平，均正常。X线检查和体层摄影术未显示任何骨骼受累情况。我们的患者在全身麻醉下接受了手术切除受累头皮区域的治疗，效果非常好。这是原发性CVG的一个典型病例。原发性头皮回旋状鱼鳞病的鉴别诊断包括厚皮性骨膜病、脑回状真皮内痣以及许多与头皮肥大和褶皱相关的继发性病症。一种相对简单的手术治疗可显著减轻头皮增厚，并避免浸渍。
