Haouas N, Colas J M
Service d'urologie, Centre hospitalier Louis Pasteur, Avenue Léon Jouhaux, 39100 Dole Cedex.
Rev Med Suisse. 2007 May 23;3(112):1334-6.
Amyloidosis constitutes a group of storage diseases concerning various proteins, classified as a function of the type of protein. Localized pseudo tumoral amyloidosis of the urinary tract is a rare affection with bladder like the most frequent localisation. In spite of contribution of computerized tomography scans and MRI, the diagnosis is always based on histological examination of cystoscopy samples. Investigations are required to eliminate a generalized amyloidosis or a malignant lymphoproliferation. Treatment should be as conservative as possible on the outside of a massive and recurrent haematuria to be able to involve vital prognosis.
淀粉样变性是一组涉及多种蛋白质的贮积病,根据蛋白质类型进行分类。泌尿道局限性假肿瘤性淀粉样变性是一种罕见疾病,膀胱是最常见的发病部位。尽管计算机断层扫描和磁共振成像有所帮助,但诊断仍始终基于膀胱镜检查样本的组织学检查。需要进行相关检查以排除全身性淀粉样变性或恶性淋巴增殖性疾病。除了大量反复血尿可能影响重要预后外,治疗应尽可能保守。