López Gútiérrez J C, de Agustín J C, Murcia J, Carrero C, Muguerza R, Soto C, Utrilla J G, Lassaletta L
Departamento de Cirugía Pediátrica, Hospital Infantil La Paz, Madrid.
Cir Pediatr. 1991 Oct;4(4):212-4.
A two-year-old male is presented. Small bowel aganglionosis was proved to extend to 3 cm below ligament of Treitz. Gastrostomy and ileostomy was done. He received his caloric intake by cyclic home parenteral nutrition trough implantable venous system. At eighteen months of age, intestinal transplantation was refused and reoperation was done. The child underwent Ziegler's miotomymiectomy on 60 cm of aganglionic jejunum. Now at twenty seven months of age he receives cyclic parenteral nutrition, and enteral feedings are being increased slowly. The weight/height was at 91 per 100 standard, intestinal motility appears much better on contrast study and he is developmentally a normal child.
现介绍一名两岁男性患儿。经证实，小肠神经节缺如延伸至屈氏韧带以下3厘米处。已实施胃造口术和回肠造口术。他通过可植入静脉系统接受周期性家庭肠外营养以获取热量摄入。18个月大时，家属拒绝了肠道移植并进行了再次手术。该患儿对60厘米无神经节空肠进行了齐格勒肌切开肌切除术。现在患儿27个月大，接受周期性肠外营养，肠内喂养正在缓慢增加。其体重/身高处于每100标准的91，对比研究显示肠道蠕动明显改善，且他在发育上是一个正常的孩子。
