一名近乎全肠道无神经节细胞症的3年幸存者。

A 3-year survivor of near-total intestinal aganglionosis.

作者信息

Zerella J T, Ingebo K R

机构信息

Department of Surgery, Phoenix Children's Hospital, AZ 85006.

出版信息

J Pediatr Surg. 1993 Dec;28(12):1589-91. doi: 10.1016/0022-3468(93)90108-w.

DOI:10.1016/0022-3468(93)90108-w

PMID:8301502

Abstract

A newborn girl had no ganglion cells beyond 2 cm distal to the ligament of Treitz. The proximal jejunum was dilated. A jejunostomy constructed 46 cm distal to the ligament of Treitz functioned. A 28-cm jejunal segment was myectomized to augment enteral feeding. For almost 1 year she has been on enteral feedings only, and her body size has been in the 75th percentile.

摘要

一名新生女婴在屈氏韧带远端2厘米以外没有神经节细胞。近端空肠扩张。在屈氏韧带远端46厘米处构建的空肠造口发挥了作用。切除了一段28厘米的空肠段以增加肠内喂养。近1年来，她一直仅接受肠内喂养，其身体尺寸处于第75百分位。