Sawatzki M, Daikeler T, Häusermann P
Medizinische Poliklinik, Universitätsspital Basel.
Praxis (Bern 1994). 2007 Jul 4;96(27-28):1087-90. doi: 10.1024/1661-8157.96.27.1087.
We present a 53 year old woman with a progressive violaceous erythema (heliotrop rash) of the face with periorbital oedema. A clinical diagnosis of dermatomyositis was proposed. Except for the cutaneous manifestation there was no further clinical evidence of systemic disease and specifically of muscle involvement. The lesions developed about six months earlier and an amyopathic dermatomyositis was diagnosed. The patient was treated with hydroxychloroquine. The risk of malignant disease is increased in primary idiopathic and amyopathic adult onset dermatomyositis. Therefore an adequate work-up is mandatory.
我们报告一名53岁女性，面部出现进行性紫罗兰色红斑（向阳疹）并伴有眶周水肿。临床拟诊为皮肌炎。除皮肤表现外，无系统性疾病尤其是肌肉受累的进一步临床证据。这些皮损约在6个月前出现，诊断为无肌病性皮肌炎。该患者接受了羟氯喹治疗。原发性特发性和无肌病性成人起病皮肌炎患者发生恶性疾病的风险增加。因此，进行充分的检查是必不可少的。
