Xu Tao, Zhao Wei Hong, Wang Xiao Feng, Huang Xiao Bo, Xu Qing Quan, Yang Bo, Ye Xiong Jun
Department of Urology, Peking University People's Hospital, Beijing 100044, China.
Beijing Da Xue Xue Bao Yi Xue Ban. 2007 Aug 18;39(4):355-60.
Two brothers presented with renal failure. CT and MRL showed bilateral hydronephrosis and hydroureters. A cystogram was performed and showed an elevated pear-shaped bladder secondary to thickening of the bladder wall. Bladder and sigmoid were surrounded by homogeneous fat tissue. The colon was symmetrically fusiform narrowed. Ileal bladder surgery was conducted. We reviewed a total of 96 studies reported between 1959 and 2005,a including 198 patients with pelvic lipomatosis. The ratio of males to females was 27:1. Pelvic lipomatosis was a rare disorder of benign mature adipose tissue proliferation around the bladder and rectum, with urological or digestive system symptoms as the chief presentation. Most cases were associated with hypertension, proliferative cystitis and upper tract obstruction. Also there were risks of thrombosis, calculi and bladder adenocarcinoma. The chief differential diagnosis was liposarcoma. Currently, urinary diversion is the main treatment to relieve urinary obstruction.
两兄弟出现肾衰竭。CT和磁共振成像显示双侧肾盂积水和输尿管积水。进行了膀胱造影，结果显示膀胱壁增厚导致膀胱呈梨形且位置抬高。膀胱和乙状结肠被均匀的脂肪组织包绕。结肠呈对称的梭形狭窄。实施了回肠膀胱手术。我们回顾了1959年至2005年间报道的总共96项研究，其中包括198例盆腔脂肪增多症患者。男女比例为27:1。盆腔脂肪增多症是一种罕见的疾病，表现为膀胱和直肠周围良性成熟脂肪组织增生，主要表现为泌尿系统或消化系统症状。大多数病例与高血压、增殖性膀胱炎和上尿路梗阻有关。此外，还存在血栓形成、结石和膀胱腺癌的风险。主要的鉴别诊断是脂肪肉瘤。目前，尿流改道是缓解尿路梗阻的主要治疗方法。
