Delplace D, da Costa L M, Goffin L, Wechsler M E, Sass U, André J, Dangoisse C, Song M
Department of Dermatology, University Hospital Saint-Pierre, Brugmann and HUDERF, Free University of Brussels, Belgium.
J Eur Acad Dermatol Venereol. 2007 Aug;21(7):969-72. doi: 10.1111/j.1468-3083.2006.02086.x.
Churg-Strauss Syndrome (CSS) is a relatively rare entity characterized by asthma, transient pulmonary infiltrates, eosinophilia and systemic vasculitis. Oral ulceration is a possible clinical manifestation of some systemic vasculitides, such as Wegener's granulomatosis (WG) or giant cell arteritis, but has never been reported with Churg-Strauss syndrome. We report the first observation of a palatine ulceration in a 15-year-old girl with Churg-Strauss syndrome.
变应性肉芽肿性血管炎(CSS)是一种相对罕见的疾病,其特征为哮喘、短暂性肺部浸润、嗜酸性粒细胞增多和系统性血管炎。口腔溃疡是一些系统性血管炎(如韦格纳肉芽肿病(WG)或巨细胞动脉炎)可能的临床表现,但变应性肉芽肿性血管炎从未有过相关报道。我们报告了首例15岁变应性肉芽肿性血管炎女孩出现腭部溃疡的观察病例。