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复发性急性胰腺炎作为囊性纤维化的一种并发症:1例手术治疗报告。

Recurrent acute pancreatitis as a complication of cystic fibrosis: report of one case treated surgically.

作者信息

Moreno González E, Ibañez Aguirre J, Rico Selas P, Vorwald P, Santoyo Santoyo J, Gómez Sanz R, Seoane González J, Figueroa Andollo J, Sciadini M

机构信息

General and Digestive Surgery Service C, University Hospital 12 de Octubre, Madrid.

出版信息

Ann Ital Chir. 1991 Jul-Aug;62(4):345-7; discussion 347-8.

PMID:1768003
Abstract

We present the case of a young woman previously diagnosed with cystic fibrosis (CF) manifested primarily by respiratory symptoms and pancreatic exocrine insufficiency. Only 0.5% of these patients suffer from episodes of recurrent acute pancreatitis, the majority of which respond to conservative treatment. In this case, recurrent episodes of acute pancreatitis made it necessary to perform a surgical pancreatic drainage procedure.

摘要

我们报告了一例先前被诊断为囊性纤维化(CF)的年轻女性病例,其主要表现为呼吸道症状和胰腺外分泌功能不全。这些患者中仅有0.5%会出现复发性急性胰腺炎发作,其中大多数对保守治疗有反应。在该病例中,复发性急性胰腺炎发作使得有必要进行手术胰腺引流术。

相似文献

1
Recurrent acute pancreatitis as a complication of cystic fibrosis: report of one case treated surgically.复发性急性胰腺炎作为囊性纤维化的一种并发症:1例手术治疗报告。
Ann Ital Chir. 1991 Jul-Aug;62(4):345-7; discussion 347-8.
2
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[Acute pancreatitis: an infrequent complication of cystic fibrosis (mucoviscidosis)].[急性胰腺炎:囊性纤维化(黏液黏稠症)的一种罕见并发症]
Rev Esp Enferm Apar Dig. 1989 May;75(5):515-8.
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Pancreatitis as initial presentation of cystic fibrosis in young adults. A report of two cases.胰腺炎作为年轻成年人囊性纤维化的首发表现。两例报告。
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[Pancreatitis in cystic fibrosis: association with genotype and pancreatic status].[囊性纤维化中的胰腺炎:与基因型和胰腺状态的关联]
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Recurrent acute pancreatitis in patients with cystic fibrosis with normal pancreatic enzymes.胰腺酶正常的囊性纤维化患者复发性急性胰腺炎
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引用本文的文献

1
Atypical presentation of acute pancreatitis in a man with pancreatic insufficiency and cystic fibrosis: a case report.一名患有胰腺功能不全和囊性纤维化男性的急性胰腺炎非典型表现:病例报告
J Med Case Rep. 2010 Aug 18;4:275. doi: 10.1186/1752-1947-4-275.
2
Recurrent acute pancreatitis: clinical profile and an approach to diagnosis.复发性急性胰腺炎:临床特征及诊断方法。
Dig Dis Sci. 2010 Dec;55(12):3610-6. doi: 10.1007/s10620-010-1175-8. Epub 2010 Mar 16.
3
Pancreatic exocrine function in patients with cystic fibrosis.囊性纤维化患者的胰腺外分泌功能
Curr Gastroenterol Rep. 2005 Jun;7(3):227-33. doi: 10.1007/s11894-005-0039-4.