Bist S S, Bisht Manisha, Varshney S, Pathak V P
Department of E.N.T, Himalayan Institute of Medical Sciences, Jolly-grant, Dehradun (UA) - 248140, India.
J Assoc Physicians India. 2007 Jun;55:445-7.
Rosai Dorfman Syndrome (RDS) is a benign condition and a rare cause of cervical lymphadenopathy. It usually occurs in the first decade of life and manifest as massive enlargement of cervical lymph nodes. The disease has a benign course and involvement of the nasal cavity as an extranodal site is exceptional. A 22-year-old male presented as progressive massive bilateral cervical lymphadenopathy accompanied with nasal obstruction and occasional episodes of epistaxis. A FNAC from cervical lymph node and biopsy from nasal mass was compatible with RDS.
罗萨伊-多夫曼综合征(RDS)是一种良性疾病,是颈部淋巴结病的罕见病因。它通常发生在生命的第一个十年,表现为颈部淋巴结的巨大肿大。该疾病病程良性,鼻腔作为结外部位受累极为罕见。一名22岁男性表现为进行性双侧颈部淋巴结巨大肿大,伴有鼻塞和偶尔的鼻出血。颈部淋巴结细针穿刺活检(FNAC)及鼻腔肿物活检结果符合罗萨伊-多夫曼综合征。