Quintero Christian, Sasken Harvey, Houck Karen L, Hernandez Enrique
Department of Obstetrics, Gynecology and Reproductive Sciences, Temple University Hospital, 3401 North Broad, Philadelphia, PA 19140, USA.
J Reprod Med. 2007 Aug;52(8):741-4.
Angiomyofibroblastoma is a rare soft tissue neoplasm that presents most frequently in the genital region of young to middle-aged women.
A 28-year-old woman presented with nausea, vomiting and pelvic pain. Computed tomography revealed a well-circumscribed, brightly enhancing pararectal mass in the retroperitoneum. A core needle biopsy suggested the diagnosis of angiofibromyoblastoma. Due to the highly vascular nature of the lesion, the patient underwent angiographically guided embolization in an effort to minimize surgical blood loss. This was followed by exploratory laparotomy and resection of the mass.
This case illustrates an unusual presentation of angiomyofibroblastoma in the pelvic retroperitoneum and its management with preoperative selective embolization, which may have contributed to the minimal blood loss at the time of resection.
血管肌纤维母细胞瘤是一种罕见的软组织肿瘤，最常出现在年轻至中年女性的生殖器区域。
一名28岁女性出现恶心、呕吐和盆腔疼痛。计算机断层扫描显示腹膜后直肠旁有一个边界清晰、强化明显的肿块。粗针活检提示血管纤维肌母细胞瘤的诊断。由于病变血管丰富，患者接受了血管造影引导下的栓塞术，以尽量减少手术中的失血。随后进行了剖腹探查并切除了肿块。
本病例说明了血管肌纤维母细胞瘤在盆腔腹膜后的一种不寻常表现及其术前选择性栓塞的治疗方法，这可能有助于在切除时减少失血。
