Maciel Júnior J A, Da Rocha C M, Cabelho S, Pradal M G
Departamento de Neurologia, Faculdade de Ciências Médicas, Universidade Estadual de Campinas (UNICAMP), Brasil.
Arq Neuropsiquiatr. 1991 Sep;49(3):342-7. doi: 10.1590/s0004-282x1991000300020.
Report of an early case of Shy-Drager syndrome in a 67 year-old woman patient. Autonomic failure was diagnosed by functional evaluation as well as laboratory tests. MR imaging disclosed a prominent putamina hypodensity in T2-weighted images at high field strength due to iron increased depositing in this basal ganglia. MR imaging evidences confirm Shy-Drager syndrome diagnosis, and contributes for differential diagnosis of idiopathic hypotension (pure autonomic failure) in special in SDS early cases.
一名67岁女性患者的Shy-Drager综合征早期病例报告。通过功能评估以及实验室检查诊断为自主神经功能衰竭。磁共振成像显示,在高场强T2加权图像上,壳核有明显低密度影,这是由于该基底节中铁沉积增加所致。磁共振成像证据证实了Shy-Drager综合征的诊断,并有助于鉴别诊断特发性低血压(纯自主神经功能衰竭),特别是在Shy-Drager综合征早期病例中。