Choi Ic Sun, Kook Hoon, Han Dong Kyun, Baek Hee Jo, Jung Sung Taek, Lee Jae Hyuk, Park Jin Gyoon, Hwang Tai Ju
Department of Pediatrics, Chonnam National University Hwasun Hospital, Chonnam National University Medical School, Gwangju, Korea.
J Pediatr Hematol Oncol. 2007 Dec;29(12):854-7. doi: 10.1097/MPH.0b013e31815815ae.
Melanotic neuroectodermal tumor of infancy (MNTI) is an uncommon neoplasm that most often affects the maxilla in the first year of life. MNTI occurring in the long bones is extremely rare, with only 2 cases reported in the medical literature. Here we report a case of MNTI in the right femur of a 5-month-old infant who underwent neoadjuvant chemotherapy followed by limb-salvage surgery.
婴儿黑色素性神经外胚层肿瘤（MNTI）是一种罕见的肿瘤，最常发生于出生后第一年的上颌骨。发生于长骨的MNTI极为罕见，医学文献中仅报道过2例。在此，我们报告1例发生于5个月大婴儿右股骨的MNTI，该患儿接受了新辅助化疗，随后进行了保肢手术。
