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非典型亚急性硬化性全脑炎:病例报告

Atypical subacute sclerosing panencephalitis: case report.

作者信息

Cruzeiro Marcelo Maroco, Vale Thiago Cardoso, Pires Leopoldo Antônio, Franco Gláucio Mendes

机构信息

Neurology Service, Department of Internal Medicine, University Hospital, Federal University of Juiz de Fora, Avenida Rio Branco 2370/802, Juiz de Fora, MG, Brazil.

出版信息

Arq Neuropsiquiatr. 2007 Dec;65(4A):1030-3. doi: 10.1590/s0004-282x2007000600024.

DOI:10.1590/s0004-282x2007000600024
PMID:18094871
Abstract

Subacute sclerosing panencephalitis (SSPE) is a progressive inflammatory disorder of the central nervous system with both poor prognosis and high mortality. The disease has been related to a persistent and aberrant measles virus infection and no effective treatment has been available. We report a case of SSPE with atypical features including seizures at onset and a fulminant course in a 8 years-old boy who had been previously immunized against measles.

摘要

亚急性硬化性全脑炎(SSPE)是一种中枢神经系统的进行性炎症性疾病,预后差且死亡率高。该疾病与持续性及异常的麻疹病毒感染有关,目前尚无有效的治疗方法。我们报告一例具有非典型特征的SSPE病例,该病例为一名8岁男孩,起病时有癫痫发作且病程呈暴发性,该男孩此前已接种过麻疹疫苗。

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Atypical subacute sclerosing panencephalitis: case report.非典型亚急性硬化性全脑炎:病例报告
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引用本文的文献

1
Subacute sclerosing panencephalitis in a child with recurrent febrile seizures.一名患有复发性热性惊厥儿童的亚急性硬化性全脑炎
Case Rep Pediatr. 2015;2015:783936. doi: 10.1155/2015/783936. Epub 2015 Feb 24.
2
Epilepsia partialis continua in children with fulminant subacute sclerosing panencephalitis.儿童暴发性亚急性硬化性全脑炎连续性部分性癫痫发作。
Neurol Sci. 2011 Dec;32(6):1007-12. doi: 10.1007/s10072-010-0442-y. Epub 2010 Oct 30.