Laparoscopic uterovaginal anastomosis in Mayer-Rokitansky-Küster-Hauser syndrome with functioning horn.

OBJECTIVE

To reestablish uterovaginal continuity using a total laparoscopic procedure in Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome with a functioning right horn.

DESIGN

Case report.

SETTING

University hospital of Hotel Dieu de Lyon.

PATIENT(S): A 13-year-old woman with cyclic abdominal pain. We diagnosed MRKH syndrome with cyclic pain due to a hematometra in a functioning right horn associated to a right hematosalpinx and a nonfunctioning left horn.

INTERVENTION(S): Reestablishing uterovaginal continuity with excision of the left rudimentary horn via a total laparoscopic procedure.

MAIN OUTCOME MEASURE(S): Restoring regular menstruation.

RESULT(S): After total laparoscopic uterovaginal anastomosis and excision of the left nonfunctioning horn, the patient's menstruation resumed 3 months later, and regular, unimpeded menstrual flow was still present at the 2-year-follow-up evaluation.

CONCLUSION(S): Total laparoscopic reestablishment of uterovaginal continuity in MRKH syndrome with a functioning horn is a valuable alternative to the currently recommended treatment (laparotomy and radical excision of the rudimentary uterus).