Department of Gynecology, the Fourth Hospital of Hebei Medical University, No.12 Health Road, Chang' an District, Shijiazhuang, 050011, Hebei, China.
BMC Womens Health. 2023 Nov 27;23(1):634. doi: 10.1186/s12905-023-02741-1.
In the past, the primary treatment for MRKH syndrome (Mayer-Rokitansky-Küster-Hauser syndrome) with a functional primordial uterus was surgical removal of the functional primordial uterus. In rare instances, the endometrium of the functional primordial uterus is well developed, and surgical preservation of the functional primordial uterus provides the possibility of preserving reproductive function for these patients.
A 14-year-old female was diagnosed with type I MRKH syndrome with a functional primordial uterus through physical examination and imaging investigations. We freed the functional primordial uterus through laparoscopic surgery and excised a portion of the lower myometrium to create an outlet at a lower uterine segment, which we then intermittently anastomosed to the tip of the artificial vagina. The patient recovered well after the surgery, and a re-examination showed no significant abnormalities.
We were successful in preserving the functional primordial uterus using laparoscopic surgery in a patient with MRKH syndrome and connecting it to an artificial vagina through reconstructive surgery to ensure unobstructed menstrual drainage and preserve the reproductive potential of the patient.
过去，对于有功能性原始子宫的 MRKH 综合征（Mayer-Rokitansky-Küster-Hauser 综合征）患者，主要的治疗方法是手术切除功能性原始子宫。在极少数情况下，功能性原始子宫的子宫内膜发育良好，手术保留功能性原始子宫为这些患者保留生育功能提供了可能。
一名 14 岁女性因体格检查和影像学检查被诊断为 I 型 MRKH 综合征伴功能性原始子宫。我们通过腹腔镜手术释放了功能性原始子宫，并切除了一部分下子宫肌层，在子宫下段创建一个出口，然后间歇性地将其与人工阴道的顶端吻合。患者术后恢复良好，复查未见明显异常。
我们成功地通过腹腔镜手术保留了 MRKH 综合征患者的功能性原始子宫，并通过重建手术将其与人工阴道相连，以确保月经血通畅排出，并保留患者的生育潜能。
