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患有复杂型 Mayer-Rokitansky-Küster-Hauser 综合征女性的巨大子宫平滑肌瘤病例报告及手术解决方案

Case report and surgical solution for a voluminous uterine leiomyoma in a woman with complicated Mayer-Rokitansky-Küster-Hauser syndrome.

作者信息

Papa Gaetano, Andreotti Maurizio, Giannubilo Stefano Raffaele, Cesari Rita, Ceré Isabella, Tranquilli Andrea Luigi

机构信息

Department of Obstetrics and Gynecology, Sacra Famiglia Hospital, Novafeltria, Italy.

出版信息

Fertil Steril. 2008 Nov;90(5):2014.e5-6. doi: 10.1016/j.fertnstert.2008.04.061.

DOI:10.1016/j.fertnstert.2008.04.061
PMID:18993169
Abstract

OBJECTIVE

To describe a case of leiomyoma in a patient with Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome.

DESIGN

Case report.

SETTING

Department of Obstetrics and Gynecology, "Sacra Famiglia Hospital," Novafeltria, Italy.

PATIENT(S): A 47-year-old woman with MRKH syndrome with lower abdominal pain and pelvic tumescence.

INTERVENTION(S): Surgery.

MAIN OUTCOME MEASURE(S): Results on ultrasound scan and magnetic resonance imaging.

RESULT(S): A pelvic leiomyoma originating from uterine remnant; resection of the mass was performed.

CONCLUSION(S): Even though magnetic resonance imaging is useful for the diagnosis of leiomyoma of the rudimentary uterus in MRKH syndrome, surgery might be the only definitive solution. Removal of the opposite uterine remnant could also be proposed.

摘要

目的

描述1例患有迈耶-罗基坦斯基-库斯特-豪泽综合征(MRKH综合征)患者的平滑肌瘤病例。

设计

病例报告。

地点

意大利诺瓦费尔特里亚“圣家族医院”妇产科。

患者

1名47岁患有MRKH综合征的女性,有下腹部疼痛和盆腔肿胀。

干预措施

手术。

主要观察指标

超声扫描和磁共振成像结果。

结果

1例起源于子宫残端的盆腔平滑肌瘤;对肿块进行了切除。

结论

尽管磁共振成像有助于诊断MRKH综合征中残角子宫的平滑肌瘤,但手术可能是唯一的确定性解决方案。也可以考虑切除对侧子宫残端。

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