Koch Moritz, Nielsen G Petur, Yoon Sam S
Department of Surgery, University of Heidelberg, Heidelberg, Germany.
J Surg Oncol. 2008 Mar 15;97(4):321-9. doi: 10.1002/jso.20973.
Sarcomas that arise from or resemble the components of blood vessels are uncommon and include angiosarcomas, hemangioendotheliomas, and hemangiopericytomas. This article reviews the management of these three types of sarcomas. Diagnosis can sometimes be difficult, with the diagnosis of hemangiopericytoma versus solitary fibrous tumor currently in debate. Each of these sarcomas subtypes has certain unique clinical traits. The mainstay of treatment is surgical resection, sometimes combined with radiation therapy. Adjuvant chemotherapy is unproven but can be considered. For patients with advanced disease, various chemotherapeutic regimens may result in meaningful responses in a minority of patients.
起源于血管成分或与之相似的肉瘤并不常见，包括血管肉瘤、血管内皮瘤和血管外皮细胞瘤。本文综述了这三种类型肉瘤的治疗方法。诊断有时会很困难，目前血管外皮细胞瘤与孤立性纤维瘤的诊断仍存在争议。这些肉瘤亚型各自具有某些独特的临床特征。治疗的主要方法是手术切除，有时联合放射治疗。辅助化疗未经证实，但可以考虑。对于晚期疾病患者，各种化疗方案可能会使少数患者产生显著疗效。
