Kaur Apjit, Kishore Poonam, Agrawal Ajai, Gupta Aparna
Department of Ophthalmology, King George's Medical University, Lucknow, India.
Orbit. 2008;27(1):63-7. doi: 10.1080/01676830601169007.
Mesenchymal chondrosarcoma, an uncommon lesion in bone and extraskeletal tissue, is extremely rare in the orbit. Two cases of orbital mesenchymal chondrosarcoma in young adults presenting with proptosis and diminution of vision are reported. The diagnosis was established by histopathological examination in both cases, which showed undifferentiated mesenchymal cells with islands of cartilage. Both patients underwent exenteration followed by chemotherapy and radiation therapy and are alive with healthy orbits after two years of follow-up.
间叶性软骨肉瘤是一种在骨骼和骨骼外组织中少见的病变,在眼眶中极为罕见。本文报告了两例发生于年轻成人的眼眶间叶性软骨肉瘤病例,患者均表现为眼球突出和视力减退。两例病例均经组织病理学检查确诊,结果显示为未分化间叶细胞伴有软骨岛。两名患者均接受了眶内容剜除术,随后进行化疗和放疗,随访两年后眼眶情况良好,患者存活。