Patel Ravija, Mukherjee Bipasha
Department of Orbit, Oculoplasty, Reconstructive & Aesthetic Services, Sankara Nethralaya, Chennai, India.
Orbit. 2012 Apr;31(2):126-8. doi: 10.3109/01676830.2011.638097.
To report a case of mesenchymal chondrosarcoma of the orbit and describe its clinical features, radiological findings and management.
Interventional case report.
A 50 year old man presented with right sided proptosis of 3 months duration. CT scan showed well circumscribed lobulated extraconal mass lesion in the inferotemporal qaudrant with specked calcification within. Patient underwent excisional biospsy with excision of mass lesion in toto. Histopathological examination was suggestive of mesenchymal chondrosarcoma of orbit. Post operatively patient was advised radiotherapy.
Orbital mesenchymal chondrosarcoma is a rare tumor characterized by undifferentiated mesenchymal cells with islands of mature hyaline cartilage. Multimodality treatment (surgery, chemotherapy, and radiotherapy) may lead to long-term survival.
报告1例眼眶间叶性软骨肉瘤病例，并描述其临床特征、影像学表现及治疗方法。
介入性病例报告。
一名50岁男性，右侧眼球突出3个月。CT扫描显示颞下象限有边界清晰的分叶状眶外肿块，内有斑点状钙化。患者接受了切除活检，完整切除了肿块。组织病理学检查提示为眼眶间叶性软骨肉瘤。术后建议患者接受放疗。
眼眶间叶性软骨肉瘤是一种罕见肿瘤，其特征为未分化的间叶细胞伴有成熟透明软骨岛。多模式治疗（手术、化疗和放疗）可能带来长期生存。
