病例报告：桥小脑角蛛网膜囊肿导致新生儿“听觉神经病”。
Case report: "auditory neuropathy" in a newborn caused by a cerebellopontine angle arachnoid cyst.
作者信息
Boudewyns A N, Declau F, De Ridder D, Parizel P M, van den Ende J, Van de Heyning P H
机构信息
Department of Otorhinolaryngology, Head and Neck Surgery, Antwerp University Hospital, University of Antwerp, Wilrijkstraat 10, 2650 Edegem, Belgium.
出版信息
Int J Pediatr Otorhinolaryngol. 2008 Jun;72(6):905-9. doi: 10.1016/j.ijporl.2008.02.003. Epub 2008 Mar 19.
We present a 6-week-old girl, referred because of failed newborn hearing screening in the right ear. Click-evoked oto-acoustic emissions were present in both ears, auditory brainstem responses (ABR) were present in the left but totally absent in the right ear. A magnetic resonance imaging (MRI) study revealed a large arachnoid cyst in the right cerebellopontine angle (CPA) and a diagnosis of "auditory neuropathy/auditory dyssynchrony" was established. A microsurgical resection of the cyst wall and fenestration was performed by a retro sigmoid approach. This is the first case in the literature of auditory neuropathy (AN) in an infant caused by a cerebellopontine angle arachnoid cyst.
我们报告一名6周大的女孩，因新生儿右耳听力筛查未通过前来就诊。双耳均存在瞬态诱发耳声发射，左耳存在听觉脑干反应（ABR），但右耳完全缺失。磁共振成像（MRI）研究显示右侧桥小脑角（CPA）有一个大的蛛网膜囊肿，并确诊为“听觉神经病/听觉失同步”。通过乙状窦后入路对囊肿壁进行了显微手术切除并开窗。这是文献中首例由桥小脑角蛛网膜囊肿引起的婴儿听觉神经病（AN）病例。
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