Foster R N, Boothroyd K P
Royal Albert Edward Infirmary, Wigan, Lancs, UK.
Anaesthesia. 2008 May;63(5):544-7. doi: 10.1111/j.1365-2044.2007.05411.x.
We describe the anaesthetic management of a 21-year-old lady with central core disease for elective Caesarean section. Central core disease is characterised by muscle weakness, skeletal deformities and susceptibility to malignant hyperthermia. Total intravenous anaesthesia was used because of the combination of potential malignant hyperthermia, severe kyphoscoliosis and extensive spinal scarring. The authors believe there is no previous report of propofol and remifentanil being used in these circumstances. A short review of central core disease and its anaesthetic implications is provided.
我们描述了一名患有中央核疾病的21岁女性行择期剖宫产的麻醉管理情况。中央核疾病的特征为肌肉无力、骨骼畸形以及对恶性高热易感。由于存在潜在的恶性高热、严重脊柱后凸侧弯以及广泛的脊柱瘢痕，故采用了全静脉麻醉。作者认为此前尚无在这些情况下使用丙泊酚和瑞芬太尼的报道。本文对中央核疾病及其麻醉相关问题进行了简要综述。
