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原发性纵隔髓脂肪瘤。

Primary mediastinal myelolipoma.

作者信息

Vaziri Mohammad, Sadeghipour Alireza, Pazooki Abdolreza, Shoolami Leila Zahedi

机构信息

Iran University of Medical Sciences, Tehran, Iran.

出版信息

Ann Thorac Surg. 2008 May;85(5):1805-6. doi: 10.1016/j.athoracsur.2007.11.023.

DOI:10.1016/j.athoracsur.2007.11.023
PMID:18442597
Abstract

Myelolipoma is a rare mesenchymal tumor composed of an admixture of fat and bone marrow-derived hematopoietic cells. It is typically an adrenal lesion, and mediastinal location is extremely unusual. We describe a 56-year-old man with nonspecific symptoms of cough and dyspnea and no underlying disease whose chest computed tomography showed a huge (25 x 15 cm) mediastinal tumor containing calcification. Surgical removal and subsequent pathologic examination of the tumor revealed myelolipoma. Primary myelolipoma should be considered in the differential diagnosis of large posterior mediastinal tumors containing calcification.

摘要

髓脂肪瘤是一种罕见的间叶组织肿瘤,由脂肪和骨髓来源的造血细胞混合组成。它通常是肾上腺病变,位于纵隔极为罕见。我们描述了一名56岁男性,有咳嗽和呼吸困难等非特异性症状,无基础疾病,其胸部计算机断层扫描显示一个巨大的(25×15厘米)纵隔肿瘤,伴有钙化。手术切除肿瘤并随后进行病理检查,结果显示为髓脂肪瘤。在鉴别诊断含有钙化的巨大后纵隔肿瘤时,应考虑原发性髓脂肪瘤。

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1
Primary mediastinal myelolipoma.原发性纵隔髓脂肪瘤。
Ann Thorac Surg. 2008 May;85(5):1805-6. doi: 10.1016/j.athoracsur.2007.11.023.
2
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An unsual symptomatic case of mediastinal myelolipoma treated by VATS approach.1例采用电视辅助胸腔镜手术(VATS)治疗的罕见纵隔髓脂肪瘤伴症状病例。
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A rare case of a multifocal extra-adrenal myelolipoma with markedly hypocellular bone marrow.一例罕见的多灶性肾上腺外骨髓脂肪瘤伴明显低细胞性骨髓。
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Thoracic myelolipoma diagnosed by endoscopic ultrasonography and fine-needle aspiration cytology.经内镜超声检查和细针穿刺细胞学检查诊断的胸段髓脂肪瘤
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Giant adrenal myelolipoma: report of a case.巨大肾上腺髓脂肪瘤:一例报告
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A case of bilateral posterior mediastinal myelolipoma.一例双侧后纵隔髓脂肪瘤。
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A rare case of co-existing adrenal and pelvic myelolipomas.一例罕见的肾上腺和盆腔髓脂肪瘤并存病例。
Radiol Case Rep. 2018 Aug 11;13(5):999-1002. doi: 10.1016/j.radcr.2018.07.008. eCollection 2018 Oct.
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Primary mediastinal myelolipoma: a case report and literature review.原发性纵隔髓脂肪瘤:一例报告并文献复习
J Thorac Dis. 2017 Mar;9(3):E219-E225. doi: 10.21037/jtd.2017.02.65.
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Myelodysplastic hematopoiesis mimicking the bone marrow in a mediastinal myelolipoma.纵隔髓脂肪瘤中模仿骨髓的骨髓发育异常造血。
Clin Case Rep. 2017 Feb 15;5(4):385-388. doi: 10.1002/ccr3.777. eCollection 2017 Apr.
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Myelolipoma of the posterior mediastinum in a patient with chronic dyserythropoietic anemia.一名患有慢性红细胞生成异常性贫血患者的后纵隔髓脂肪瘤。
Autops Case Rep. 2016 Sep 30;6(3):35-39. doi: 10.4322/acr.2016.047. eCollection 2016 Jul-Sep.
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Mesenchymal tumours of the mediastinum--part I.纵隔间叶组织肿瘤——第一部分
Virchows Arch. 2015 Nov;467(5):487-500. doi: 10.1007/s00428-015-1830-8. Epub 2015 Sep 10.
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Intrapulmonary myelolipoma and its computed tomography features: A case report and literature review.肺内髓脂肪瘤及其计算机断层扫描特征:病例报告与文献综述
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Primary myelolipoma in posterior mediastinum.后纵隔原发性髓性脂肪瘤。
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