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原发性纵隔髓脂肪瘤:一例报告并文献复习

Primary mediastinal myelolipoma: a case report and literature review.

作者信息

Shi Qingtong, Pan Shu, Bao Yang, Fan Huangxin, Diao Yali

机构信息

Department of Cardiothoracic Surgery, The First People's Hospital of Yangzhou, Yangzhou 225000, China.

Department of Cardiothoracic Surgery, The Affiliated Hospital of Yangzhou University, Yangzhou University, Yangzhou 225000, China.

出版信息

J Thorac Dis. 2017 Mar;9(3):E219-E225. doi: 10.21037/jtd.2017.02.65.

DOI:10.21037/jtd.2017.02.65
PMID:28449507
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5393995/
Abstract

Myelolipoma is a kind of rare benign tumour composed of mature adipocytes and hemopoietic elements, and is most often found in the adrenal glands. Primary mediastinal myelolipoma (PMM) more rarely happens and has no definite symptoms, and mediastinal masses are usually found in chest examination. The patients normally receive a surgical resection and have a favorable prognosis after postoperative pathological diagnosis. Here, we present the case of PMM, which was resected via video-assisted thoracic surgery (VATS), and investigate recent correlative literatures to summarize its etiology, histopathology, differential diagnosis and therapeutic method. In this way, we aim to improve clinical doctors' understanding of this disease.

摘要

髓脂肪瘤是一种由成熟脂肪细胞和造血成分组成的罕见良性肿瘤,最常发生于肾上腺。原发性纵隔髓脂肪瘤(PMM)更为罕见,且无明确症状,纵隔肿块通常在胸部检查时被发现。患者通常接受手术切除,术后病理诊断后预后良好。在此,我们报告一例通过电视辅助胸腔镜手术(VATS)切除的PMM病例,并检索近期相关文献以总结其病因、组织病理学、鉴别诊断及治疗方法。通过这种方式,我们旨在提高临床医生对该疾病的认识。

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本文引用的文献

1
Myelolipoma of the posterior mediastinum in a patient with chronic dyserythropoietic anemia.一名患有慢性红细胞生成异常性贫血患者的后纵隔髓脂肪瘤。
Autops Case Rep. 2016 Sep 30;6(3):35-39. doi: 10.4322/acr.2016.047. eCollection 2016 Jul-Sep.
2
Mediastinal myelolipoma showing gradual enlargement over 9 years: a case report.纵隔髓脂肪瘤9年间逐渐增大:一例报告
J Cardiothorac Surg. 2016 Jun 7;11(1):91. doi: 10.1186/s13019-016-0482-3.
3
Video-assisted thoracic surgery for primary myelolipoma of the posterior mediastinum.电视辅助胸腔镜手术治疗后纵隔原发性髓脂肪瘤
J Cardiothorac Surg. 2016 Jan 13;11:1. doi: 10.1186/s13019-016-0401-7.
4
Surgical treatment of primary mediastinal myelolipoma.原发性纵隔髓脂肪瘤的外科治疗
Interact Cardiovasc Thorac Surg. 2015 Aug;21(2):206-10. doi: 10.1093/icvts/ivv112. Epub 2015 May 2.
5
Primary myelolipoma in posterior mediastinum.后纵隔原发性髓性脂肪瘤。
J Thorac Dis. 2014 Sep;6(9):E181-7. doi: 10.3978/j.issn.2072-1439.2014.07.34.
6
A bilateral neoplasm in chest: a case report and literature review.胸部双侧肿瘤:一例病例报告及文献综述
BMC Surg. 2014 Jul 9;14:42. doi: 10.1186/1471-2482-14-42.
7
Bilateral video-assisted thoracoscopic surgery resection for multiple mediastinal myelolipoma: report of a case.双侧电视辅助胸腔镜手术切除多发纵隔髓脂肪瘤:一例报告
Korean J Thorac Cardiovasc Surg. 2014 Apr;47(2):189-92. doi: 10.5090/kjtcs.2014.47.2.189. Epub 2014 Apr 10.
8
An unsual symptomatic case of mediastinal myelolipoma treated by VATS approach.1例采用电视辅助胸腔镜手术(VATS)治疗的罕见纵隔髓脂肪瘤伴症状病例。
Ann Ital Chir. 2014 Jan-Feb;85(1):85-7.
9
Mediastinal myelolipoma with leukocytosis.纵隔髓脂肪瘤伴白细胞增多症。
BMJ Case Rep. 2013 Jun 21;2013:bcr2013010349. doi: 10.1136/bcr-2013-010349.
10
Primary mediastinal myelolipoma: A case report and review of the literature.原发性纵隔髓脂肪瘤:一例报告并文献复习
Oncol Lett. 2013 Mar;5(3):862-864. doi: 10.3892/ol.2012.1085. Epub 2012 Dec 19.