Anwar Ashraf M, McGhie Jackie S, Meijboom Folkert J, Ten Cate Folkert J
Department of Cardiology, Thoraxcenter, Erasmus MC, Dr Molewaterplein 40, 3015 GD Rotterdam, The Netherlands.
Eur J Echocardiogr. 2008 Sep;9(5):731-2. doi: 10.1093/ejechocard/jen149. Epub 2008 May 1.
Double orifice mitral valve (DOMV) is a rare congenital malformation described as division of mitral orifice into two anatomically distinct orifices separated by an accessory bridge of fibrous tissue. In 85% of cases, both orifices are unequal in size. It is usually associated with other congenital defects such as atrioventricular septal defect and complex congenital heart disease. Most of cases could be diagnosed by two-dimensional echocardiography (2DE). The real-time three-dimensional echocardiography (RT3DE) helped in more detailed structure and function. Presented here RT3DE used for orientation of DOMV that allowed detailed and comprehensive assessment incremental to that obtained by 2DE.
双孔二尖瓣（DOMV）是一种罕见的先天性畸形，其特征为二尖瓣口被纤维组织的副桥分隔成两个解剖学上不同的孔口。在85%的病例中，两个孔口大小不等。它通常与其他先天性缺陷相关，如房室间隔缺损和复杂先天性心脏病。大多数病例可通过二维超声心动图（2DE）诊断。实时三维超声心动图（RT3DE）有助于更详细地了解其结构和功能。本文展示了RT3DE用于DOMV的定位，从而能够对其进行比2DE更详细和全面的评估。
