Ghirardo V, Cecchetto G, Minucci D, Dall'Igna P, De Corti F, Zanon G F
Department of Pediatrics, University Hospital of Padua, Padova.
Pediatr Med Chir. 2008 Jan-Feb;30(1):41-4.
Müllerian malformations represent a wide spectrum of anomaly of the female reproductive tract, usually detected at birth or at puberty. The presence of uterus didelphys and obstructed hemivagina, associated with ipsilateral renal agenesis, is known as Herlyn-Werner-Wunderlich syndrome, a rare congenital anomaly. Two cases of uterus didelphic and hematometra caused by vaginal septum are reported; the girls had a delayed diagnosis due to absence of a specific clinical feature. Clinicians must be aware of the existence of these malformations. An adequate radiological study is mandatory to assess the anatomic conformation, and to optimize the therapeutic procedures.
苗勒管畸形代表了女性生殖道的一系列广泛异常,通常在出生时或青春期被发现。双子宫并伴有梗阻性半阴道,同时合并同侧肾缺如,被称为赫林-韦纳-温德利希综合征,这是一种罕见的先天性异常。本文报告了两例因阴道纵隔导致的双子宫和子宫积血病例;由于缺乏特异性临床特征,这两名女孩的诊断有所延迟。临床医生必须意识到这些畸形的存在。进行充分的影像学检查对于评估解剖结构和优化治疗方案是必不可少的。