Piccinini Pedro Salomao, Doski John
Department of Surgery, University of Texas Health Science Center, San Antonio, TX, USA.
Children's Hospital of San Antonio, San Antonio, TX, USA.
Rev Bras Ginecol Obstet. 2015 Apr;37(4):192-6. doi: 10.1590/SO100-720320150005077.
Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital disorder of the Müllerian ducts in which there is uterus didelphys, obstructed hemivagina and unilateral renal agenesis. The most common presentation is an abdominal mass secondary to hematocolpos, pain and dysmenorrhea. However, in some cases, such as the one we present here, menses are normal due to an obstructed hemivagina, and diagnosis can be delayed. We describe evaluation and surgical management of a 13-year-old girl with this condition who was diagnosed by computed tomography (CT) scan and confirmed by pelvic ultrasound and surgical exploration, as well as a review of the literature.
赫林-韦纳-温德利希（HWW）综合征是一种罕见的苗勒管先天性疾病，其特征为双子宫、半阴道梗阻和单侧肾缺如。最常见的表现是因阴道积血继发的腹部肿块、疼痛和痛经。然而，在某些情况下，比如我们在此呈现的病例，由于半阴道梗阻，月经正常，诊断可能会延迟。我们描述了一名患有该疾病的13岁女孩的评估和手术治疗情况，该病例通过计算机断层扫描（CT）诊断，经盆腔超声和手术探查得以确诊，同时还对相关文献进行了综述。
