Pantaleo Antonella, Giribaldi Giuliana, Mannu Franca, Arese Paolo, Turrini Franco
Department of Genetics, Biology and Biochemistry, University of Torino, Italy.
Autoimmun Rev. 2008 Jun;7(6):457-62. doi: 10.1016/j.autrev.2008.03.017. Epub 2008 Apr 21.
Naturally occurring antibodies (NAbs) directed to band 3 protein (major erythrocyte membrane protein) are involved in the clearance of red blood cell (RBC) at the end of their lifespan as well as in the removal of RBC in different hereditary haemolytic disorders and in malaria. In all cited situations RBC undergoes oxidative stress and hemichromes (haemoglobin degradation products) are formed. Hemichromes possess a strong affinity for band 3 cytoplasmic domain and, following their binding, lead to band 3 oxidation and clusterisation. Those band 3 clusters show increased affinity for NAbs which activate complement and finally trigger the phagocytosis of altered RBC. During intra-erythrocytic malaria parasite growth, NAbs begin to bind to RBC surface at early parasite development stages increasing their abundance in parallel with parasite development. Interestingly, a number of hereditary haemolytic disorders, known to exert a protective effect on malaria, tend to exacerbate this phenomenon leading to a more precocious and effective opsonization of diseased RBC infected by malaria parasites. The exact definition of band 3 neo-antigens and the mechanism of their surface exposure are still unclear. Also band 3 clusterisation is only superficially understood, new insights about band 3 phosphorylation by Src kinases suggest the presence of a complex regulatory pathway.
针对带3蛋白(主要红细胞膜蛋白)的天然抗体(NAbs)在红细胞(RBC)寿命结束时参与其清除过程,以及在不同遗传性溶血性疾病和疟疾中参与红细胞的清除。在所有上述情况下,红细胞都会经历氧化应激并形成半色素(血红蛋白降解产物)。半色素对带3细胞质结构域具有很强的亲和力,结合后会导致带3氧化和聚集。那些带3聚集体对天然抗体的亲和力增加,天然抗体激活补体并最终触发对改变的红细胞的吞噬作用。在红细胞内疟原虫生长期间,天然抗体在寄生虫发育早期开始与红细胞表面结合,并随着寄生虫的发育而增加其丰度。有趣的是,一些已知对疟疾有保护作用的遗传性溶血性疾病往往会加剧这种现象,导致被疟原虫感染的患病红细胞更早且更有效地被调理吞噬。带3新抗原的确切定义及其表面暴露机制仍不清楚。此外,对带3聚集的理解也只是表面的,关于Src激酶对带3磷酸化的新见解表明存在复杂的调节途径。