Le Corre Y, Avenel-Audran M, Croué A, Steff M, Verret J-L
Service de dermatologie, faculté de médecine, université d'Angers, CHU d'Angers, 4, rue Larrey, 49933 Angers cedex 09, France.
Ann Dermatol Venereol. 2008 Jun-Jul;135(6-7):488-91. doi: 10.1016/j.annder.2007.08.006. Epub 2008 Apr 14.
Cutaneous angiosarcoma is a rare aggressive vascular neoplasm with a poor prognosis, seen chiefly in elderly subjects and usually on the scalp or face. The present case is original because of its localization on the leg without any chronic lymphoedema and because of the long survival period. The treatment modalities are discussed.
An 87-year-old woman presented with a rapidly growing large deep-purple ulcerated tumour on the anterior aspect of the leg. In addition, two nodules with a similar aspect appeared on the outer surface of the foot. Histological examination showed vascular channels lined with atypical cells consistent with a diagnosis of angiosarcoma. Computed tomography revealed no metastases. Amputation was performed at the thigh and there was no recurrence 30 months later.
The leg is a rare site of cutaneous angiosarcoma. Treatment usually consists of surgical excision with wide margins followed by radiotherapy, but in some cases amputation is unavoidable.
皮肤血管肉瘤是一种罕见的侵袭性血管肿瘤，预后较差，主要见于老年患者，通常发生于头皮或面部。本病例具有独特性，因其位于腿部且无任何慢性淋巴水肿，并且生存期较长。文中讨论了其治疗方式。
一名87岁女性患者，其小腿前部出现一个迅速生长的、大的深紫色溃疡性肿瘤。此外，足部外表面出现了两个外观相似的结节。组织学检查显示血管通道内衬非典型细胞，符合血管肉瘤的诊断。计算机断层扫描未发现转移。在大腿处进行了截肢手术，30个月后未出现复发。
腿部是皮肤血管肉瘤的罕见发病部位。治疗通常包括广泛切除手术，随后进行放疗，但在某些情况下截肢是不可避免的。
