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普通可变免疫缺陷综合征中的闭塞性细支气管炎并机化性肺炎

Bronchiolitis obliterans organizing pneumonia in common variable immunodeficiency syndrome.

作者信息

Kaufman J, Komorowski R

机构信息

Department of Medicine, Medical College of Wisconsin, Milwaukee.

出版信息

Chest. 1991 Aug;100(2):552-3. doi: 10.1378/chest.100.2.552.

DOI:10.1378/chest.100.2.552
PMID:1864136
Abstract

A 26-year-old woman with common variable immunodeficiency syndrome (CVID) associated with frequent episodes of pneumonia underwent an open lung biopsy showing bronchiolitis obliterans organizing pneumonia (BOOP). Following corticosteroid therapy, there were no further episodes of pneumonia. In addition, there was roentgenographic and gas exchange improvement. This is the first case of BOOP in association with CVID. An immunologic basis of BOOP is postulated.

摘要

一名26岁患有常见可变免疫缺陷综合征(CVID)且频繁发生肺炎的女性接受了开胸肺活检,结果显示为闭塞性细支气管炎并机化性肺炎(BOOP)。接受皮质类固醇治疗后,未再出现肺炎发作。此外,影像学和气体交换情况有所改善。这是首例与CVID相关的BOOP病例。推测BOOP存在免疫学基础。

相似文献

1
Bronchiolitis obliterans organizing pneumonia in common variable immunodeficiency syndrome.普通可变免疫缺陷综合征中的闭塞性细支气管炎并机化性肺炎
Chest. 1991 Aug;100(2):552-3. doi: 10.1378/chest.100.2.552.
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Bronchiolitis obliterans organizing pneumonia caused by Plasmodium vivax malaria.间日疟原虫疟疾引起的闭塞性细支气管炎并机化性肺炎
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[A case of bronchiolitis obliterans organizing pneumonia associated with ulcerative colitis].[1例与溃疡性结肠炎相关的闭塞性细支气管炎并机化性肺炎]
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Differential diagnosis of bronchiolitis obliterans organizing pneumonia.闭塞性细支气管炎伴机化性肺炎的鉴别诊断。
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Bronchiolitis obliterans organizing pneumonia and rheumatoid arthritis.闭塞性细支气管炎伴机化性肺炎与类风湿关节炎。
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Bronchiolitis obliterans organizing pneumonia associated with massive L-tryptophan ingestion.
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Pathologic manifestations of bronchiolitis, constrictive bronchiolitis, cryptogenic organizing pneumonia, and diffuse panbronchiolitis.细支气管炎、缩窄性细支气管炎、隐源性机化性肺炎及弥漫性泛细支气管炎的病理表现。
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[Bronchiolitis obliterans organizing pneumonia].[闭塞性细支气管炎并机化性肺炎]
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[Two cases of bronchiolitis obliterans organizing pneumonia, showing multiple infiltrative shadows, diagnosed by open lung biopsy, and a report of their BAL findings].[两例闭塞性细支气管炎伴机化性肺炎,表现为多发浸润影,经开胸肺活检确诊,并报告其支气管肺泡灌洗结果]
Nihon Kyobu Shikkan Gakkai Zasshi. 1990 Jan;28(1):143-50.

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