Kanu Adaobi, Tegay David, Scriven Richard
Department of Pediatrics, Texas Tech University, HSC, Lubbock, Texas, USA.
Pediatr Pulmonol. 2008 Sep;43(9):930-2. doi: 10.1002/ppul.20827.
VACTERL association is an acronym made of associated defects including vertebral anomalies, anal atresia, cardiac, tracheal-esophageal fistula, and renal/radial limb anomalies. Tracheal bronchus is a condition characterized by ectopic location of the right upper lobe bronchus at the mid to distal trachea. This condition is associated with congenital anomalies and has been reported in one previous case of VACTERL. We report another infant with VACTERL presenting with respiratory complications due to presence of tracheal bronchus. She also had a narrowed segment of her right main stem bronchus.
VACTERL综合征是一个首字母缩略词，代表一系列相关缺陷，包括脊柱异常、肛门闭锁、心脏、气管食管瘘以及肾脏/桡骨肢体异常。气管支气管是一种以上叶右支气管异位至气管中下段为特征的病症。该病症与先天性异常相关，此前曾在1例VACTERL综合征病例中被报道。我们报告了另一例患有VACTERL综合征的婴儿，因气管支气管的存在而出现呼吸并发症。她的右主支气管也有一段狭窄。
