Gupta Rahul K, Jadhav Vinay, Gupta Abhaya, Sanghvi Beejal, Shah Hemanshi, Parelkar Sandesh
Department of Pediatric Surgery, King Edward Memorial Hospital, Parel, Mumbai 400012, India.
J Pediatr Surg. 2008 Aug;43(8):1421-5. doi: 10.1016/j.jpedsurg.2007.12.072.
Congenital fusion of the jaws is rare. It may be unilateral or bilateral and may involve only the soft tissues or both the hard and soft tissues. This anomaly may be seen separately or in association with other syndromes. Congenital alveolar fusion restricts mouth opening, causing problems with feeding, swallowing, and respiration. Case 1 had membranous bands between the alveoli that required tracheostomy for stabilization, followed by osteotomy for release. Postoperatively, both patients had adequate mouth opening.
先天性颌骨融合较为罕见。它可以是单侧或双侧的,可能仅累及软组织,也可能同时累及硬组织和软组织。这种异常情况可单独出现,也可与其他综合征合并出现。先天性牙槽融合会限制张口,导致喂养、吞咽和呼吸方面的问题。病例1的牙槽之间有膜状带,需要进行气管切开术以稳定病情,随后进行截骨术以松解。术后,两名患者的张口情况均良好。