Kerr H D, Keep J C, Chiu S
Department of Medicine, Medical College of Wisconsin, Milwaukee.
South Med J. 1991 Aug;84(8):1039-41. doi: 10.1097/00007611-199108000-00024.
A man with Maffucci's syndrome and lifelong lymphedema in the right lower extremity had a lymphangiosarcoma in the same extremity. Despite amputation of the limb and radiotherapy, he died several months later of pulmonary metastases. Malignancies of vascular origin rarely have been reported in this syndrome. Our patient's features suggest that lymphedema may predispose patients with Maffucci's syndrome to the development of lymphangiosarcoma.
一名患有马富西综合征且右下肢存在终身性淋巴水肿的男性，在同一肢体发生了淋巴管肉瘤。尽管进行了截肢手术和放射治疗，但他在几个月后因肺转移而死亡。血管源性恶性肿瘤在该综合征中鲜有报道。我们患者的特征表明，淋巴水肿可能使马富西综合征患者易患淋巴管肉瘤。
