Girnita Leonard, Sahlin Sven, Orrego Abiel, Seregard Stefan
Department of Oncology and Pathology, Karolinska Institute and Karolinska University Hospital, Stockholm, Sweden.
Acta Ophthalmol. 2009 Jun;87(4):464-7. doi: 10.1111/j.1755-3768.2008.01290.x. Epub 2008 Sep 24.
We aimed to report a case of orbital solitary fibrous tumour (SFT) in a child and to review the relevant literature.
We describe an SFT in a 13-year-old boy with a 1-month history of painless proptosis in the left eye.
Magnetic resonance imaging revealed a well circumscribed mass filling most of the left intraconal orbit. The lesion was excised and histopathological examination revealed a malignant SFT. Postoperative follow-up for 18 months was uneventful.
Malignant SFT of the orbit should be included in the differential diagnosis of paediatric orbital tumours. Complete surgical excision remains the preferred method of management and the longterm prognosis is guarded.
我们旨在报告一例儿童眼眶孤立性纤维瘤（SFT）病例并复习相关文献。
我们描述了一名13岁男孩的SFT，其左眼有无痛性眼球突出1个月病史。
磁共振成像显示一个边界清晰的肿块，占据了大部分左侧肌锥内眼眶。病变被切除，组织病理学检查显示为恶性SFT。术后随访18个月无异常。
眼眶恶性SFT应纳入小儿眼眶肿瘤的鉴别诊断。完整的手术切除仍然是首选的治疗方法，长期预后尚不确定。
