Klein N, Enk A, Hartschuh W
Universitäts-Hautklinik Heidelberg, Vossstrasse 2, 69115, Heidelberg, Deutschland.
Hautarzt. 2009 May;60(5):420-3. doi: 10.1007/s00105-008-1639-3.
The inflammatory stage of disseminated superficial porokeratosis is a rare disease, which has only been described in case reports, primarily affecting Japanese patients. After having asymptomatic disseminated superficial porokeratosis for years, a typical patient then experiences a sudden exacerbation with distinct pruritus. Histologically, the lesions may show eosinophilic spongiosis in addition to the characteristic cornoid lamella. We describe a 71-year old patient with clinically and histologically diagnosed inflammatory stage of disseminated superficial porokeratosis.
播散性浅表性光化性角化病的炎症期是一种罕见疾病,仅在病例报告中有描述,主要影响日本患者。在多年患有无症状的播散性浅表性光化性角化病后,典型患者会突然病情加重并伴有明显瘙痒。组织学上,除特征性的鸡眼样板层外,病变还可能显示嗜酸性海绵形成。我们描述了一名71岁临床上和组织学上诊断为播散性浅表性光化性角化病炎症期的患者。