Wells Rebecca G
Department of Medicine (Gastroenterology), University of Pennsylvania School of Medicine, Philadelphia, PA 19104-6140, USA.
Clin Liver Dis. 2008 Nov;12(4):759-68, viii. doi: 10.1016/j.cld.2008.07.008.
The deposition of increased and abnormal extracellular matrix is the hallmark of liver fibrosis. Hepatic stellate cells are well known as the major source of the fibrillar collagens and other components of the liver scar, but are now appreciated to be only one of many potentially fibrogenic cell populations in the diseased liver. Portal fibroblasts and circulating mesenchymal cells derived from the bone marrow are also important sources of matrix proteins in fibrosis. Recent data suggest that hepatocytes and biliary epithelial cells undergo an epithelial to mesenchymal transition, similarly assuming a fibrogenic phenotype. Sinusoidal endothelial cells and hepatocytes produce specific matrix proteins important in liver health and disease. The future challenge will be to define more explicitly the roles of these different fibrogenic cell populations in fibrosis in a disease-specific way.
细胞外基质增多和异常沉积是肝纤维化的标志。肝星状细胞是肝脏瘢痕中纤维状胶原蛋白和其他成分的主要来源,这一点广为人知,但现在人们认识到,它们只是患病肝脏中众多潜在致纤维化细胞群体之一。门静脉成纤维细胞和源自骨髓的循环间充质细胞也是纤维化过程中基质蛋白的重要来源。最近的数据表明,肝细胞和胆管上皮细胞会经历上皮-间质转化,同样呈现出致纤维化表型。肝窦内皮细胞和肝细胞产生对肝脏健康和疾病至关重要的特定基质蛋白。未来的挑战将是以疾病特异性的方式更明确地界定这些不同致纤维化细胞群体在纤维化中的作用。