Szili-Torok Tamas, Jessurun Emile, Jordaens Luc J
Department of Clinical Electrophysiology, Erasmus Medical Centre, Rotterdam, The Netherlands.
Acta Cardiol. 2008 Oct;63(5):647-50. doi: 10.2143/AC.63.5.2033236.
Patients with Ehlers-Danlos syndrome type IV have thin-walled, friable arteries and veins. Invasive procedures carry a significantly increased risk for perforation of blood vessels. The aim of this case report is to demonstrate the feasibility and potential benefits of using a stereotactic magnetic navigation system (MNS) for mapping and ablation under these very special circumstances. A 45-year-old woman is presented with daily episodes of typical atrio-ventricular nodal re-entry tachycardias (AVNRT) and known Ehlers-Danlos syndrome type IV. Transcatheter ablation procedure of the AVNRT was undertaken using the MNS, with a non-traumatic single floppy catheter and the capability of advanced navigation.
患有IV型埃勒斯-当洛综合征的患者动脉和静脉壁薄且脆弱。侵入性操作会显著增加血管穿孔的风险。本病例报告的目的是证明在这些非常特殊的情况下，使用立体定向磁导航系统（MNS）进行标测和消融的可行性及潜在益处。本文介绍了一名45岁女性，她每天都会发作典型的房室结折返性心动过速（AVNRT），且患有IV型埃勒斯-当洛综合征。使用MNS、非创伤性单弯导管并具备先进导航功能，对该患者进行了AVNRT的经导管消融手术。
