Meyer Sonali R, Smith Kenneth M, Ravish Indupur R, Saltzman Daniel A, Shukla Aseem R
Division of Pediatric Urology, University of Minnesota, Children's Hospital Fairview, Minneapolis, Minnesota 55123, USA.
Urology. 2009 Mar;73(3):532-4. doi: 10.1016/j.urology.2008.09.046. Epub 2008 Nov 26.
Urorectal septum malformation sequences are rare congenital malformations. We report a case of persistent cloaca prenatally diagnosed at 26 weeks of gestation in 1 of a set of discordant monozygotic twins. The affected fetus at birth had a phallus-like structure, bladder outlet obstruction, an imperforate anus, and uterine distension. Diverting colostomy, vesicostomy, and percutaneous colpostomy tube were initially placed before definitive posterior sagittal anorectovaginoplasty was completed. A cloacal anomaly occurring in only 1 of a set of monozygotic twins is an exceedingly rare event.
