Chen Feng
Renal Division, Department of Internal Medicine, Department of Cell Biology and Physiology, Washington University School of Medicine, St. Louis, MO 63110, USA.
Pediatr Nephrol. 2009 Sep;24(9):1621-32. doi: 10.1007/s00467-008-1072-y. Epub 2008 Dec 16.
Urinary tract obstruction results in obstructive nephropathy and uropathy. It is the most frequent cause of renal failure in infants and children. In the past two decades studies of transgenic models and humans have greatly enhanced our understanding of the genetic factors and developmental processes important in urinary tract obstruction. The emerging picture is that development of the urinary tract requires precise integration of a variety of progenitor cell populations of different embryonic origins. Such integration is controlled by an intricate signaling network that undergoes dynamic changes as the embryo develops. Most congenital forms of urinary tract obstruction result from the disruption of diverse factors and genetic pathways involved in these processes, especially in the morphogenesis of the urinary conduit or the functional aspects of the pyeloureteral peristaltic machinery.
尿路梗阻会导致梗阻性肾病和尿路病。它是婴幼儿肾衰竭最常见的原因。在过去二十年中,对转基因模型和人类的研究极大地增进了我们对尿路梗阻中重要的遗传因素和发育过程的理解。新出现的情况是,尿路的发育需要精确整合来自不同胚胎起源的各种祖细胞群。这种整合由一个复杂的信号网络控制,该网络随着胚胎发育而发生动态变化。大多数先天性尿路梗阻形式是由于参与这些过程的各种因素和遗传途径受到破坏,特别是在尿路管道的形态发生或肾盂输尿管蠕动机制的功能方面。