Lachkar R, Ibrahimy W, Benharbit M, Charif Chefchaouni M, Hssissen N, Lezrek M, Karim A, Benchrif Z, Daoudi R
Service d'Ophtalmologie A de l'hôpital des spécialités de Rabat, Maroc.
Bull Soc Belge Ophtalmol. 2008(309-310):31-6.
Langerhan's cell Histiocytosis of the orbit. Langerhan's cell Histiocytosis is a rare condition that affects children and less frequently young adults. It is characterized by a proliferation of histiocytes derived from Langerhan's cells. Orbital involvement is described in 20% of cases where orbital eosinophilic granuloma located in the frontal bone is the most frequent. The malignant nature of this disease is not established. Its evolution is unpredictable and spontaneous regression after simple biopsy were described. The authors report four cases of Langerhan's cell Histiocytosis and will discuss on the clinical and radiological aspects as well as on the evolution of orbital histiocytoses X.
眼眶朗格汉斯细胞组织细胞增多症。朗格汉斯细胞组织细胞增多症是一种罕见疾病，多见于儿童，较少见于年轻人。其特征是源自朗格汉斯细胞的组织细胞增殖。20%的病例有眼眶受累，其中位于额骨的眼眶嗜酸性肉芽肿最为常见。该疾病的恶性性质尚未明确。其病程不可预测，有报道称在简单活检后可自发消退。作者报告了4例朗格汉斯细胞组织细胞增多症病例，并将讨论眼眶组织细胞增多症X的临床、放射学表现以及病程。
