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外耳道肺泡状横纹肌肉瘤:一例报告

Alveolar rhabdomyosarcoma on the external ear: a case report.

作者信息

Ragsdale Bruce D, Lee Jessica P, Mines Jill

机构信息

Western Dermatopathology Services, San Luis Obispo, CA 93401, USA.

出版信息

J Cutan Pathol. 2009 Feb;36(2):267-9. doi: 10.1111/j.1600-0560.2008.01031.x.

DOI:10.1111/j.1600-0560.2008.01031.x
PMID:19208077
Abstract

Alveolar rhabdomyosarcoma (RMS) is the most common soft tissue sarcoma of childhood. It typically has middle ear/temporal bone and nasopharynx as its most common head and neck sites. In fact, 'middle ear' is what is meant by 'ear' location in the many reports of pediatric RMS. This case report, however, is of RMS occurring on the external ear of a young female. RMS in skin should motivate a search for an occult extremity or visceral tumor, which was not present in this case.

摘要

肺泡横纹肌肉瘤(RMS)是儿童期最常见的软组织肉瘤。它通常以中耳/颞骨和鼻咽部为头颈部最常见的发病部位。实际上,在许多儿童RMS的报告中,“中耳”就是“耳部”位置的含义。然而,本病例报告是关于一名年轻女性外耳发生的RMS。皮肤发生RMS时应排查是否存在隐匿性四肢或内脏肿瘤,本病例中未发现此类情况。

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引用本文的文献

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Pediatric Patient with Rhabdomyosarcoma Involving Temporal Bone: Case Report and Overview of Recent Cases.儿童横纹肌肉瘤累及颞骨:病例报告及近期病例概述。
Am J Case Rep. 2022 Dec 9;23:e937307. doi: 10.12659/AJCR.937307.
2
Treatment, Survival, and Demographics in Temporal Bone Malignancies: A Pooled Data Analysis.颞骨恶性肿瘤的治疗、生存情况及人口统计学特征:一项汇总数据分析
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