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实时三维超声心动图诊断双心室心肌致密化不全心肌病

Diagnosis of biventricular non-compaction cardiomyopathy by real-time three-dimensional echocardiography.

作者信息

Nemes Attila, Caliskan Kadir, Soliman Osama I I, McGhie Jackie S, Geleijnse Marcel L, ten Cate Folkert J

机构信息

Department of Cardiology, Thoraxcentre, Erasmus MC, Dr Molewaterplein 40, 3015 GD, Room Ba304, Rotterdam, The Netherlands.

出版信息

Eur J Echocardiogr. 2009 Mar;10(2):356-7. doi: 10.1093/ejechocard/jep008. Epub 2009 Feb 12.

DOI:10.1093/ejechocard/jep008
PMID:19213803
Abstract

Non-compaction of the ventricular myocardium is a recently recognized rare disorder of the endomyocardial morphogenesis. The disease can be characterized by systolic and diastolic heart failure, ventricular arrhythmias and systemic embolization. The present case suggests the clinical role of real-time three-dimensional echocardiography in the spatial evaluation of both ventricles in suspected biventricular non-compaction cardiomyopathy.

摘要

心室心肌致密化不全是一种最近才被认识到的罕见的心内膜心肌形态发生障碍性疾病。该疾病的特征可以表现为收缩性和舒张性心力衰竭、室性心律失常以及全身栓塞。本病例提示了实时三维超声心动图在疑似双心室心肌致密化不全心肌病患者双心室空间评估中的临床作用。

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