Wei Bo, Wei Hong-Bo, Guo Wei-Ping, Zheng Zong-Heng, Huang Yong, Hu Bao-Guang, Huang Jiang-Long
Department of Gastrointestinal Surgery, the Third Affiliated Hospital of Sun Yat-Sen University, Guangzhou, China.
Am J Surg. 2009 Sep;198(3):348-53. doi: 10.1016/j.amjsurg.2008.07.054. Epub 2009 Feb 13.
Abdominal cocoon (AC) is a rare disease characterized by total or partial encasement of the small bowel by a thick, fibrous membrane. Twenty-four cases are reported in this article. Our aim was to investigate the methods of diagnosis and treatment for AC.
The clinical manifestations, diagnoses, surgical treatments, and follow-up results of 24 cases of AC in the Department of General Surgery of the Third Affiliated Hospital of Sun Yat-sen University between January 1997 and September 2007 were retrospectively analyzed.
Main clinical manifestations were partial or complete intestinal obstruction (87.5%) and abdominal mass (54.2%). Three cases were preoperatively diagnosed by computed axial tomography and 1 case by barium x-ray examination. The other 20 cases were diagnosed by laparotomy. All of the patients underwent surgery. In all cases, we found that part of or the entire small bowel was encapsulated in a dense, white, fibrous, cocoon-like membrane. During surgery, excision of the thick membrane and lysis of adhesions were carefully performed to release the small intestine. Postsurgical recovery in most cases was smooth, and there was no recurrence during a follow-up period of 3 months to 9 years (mean 37 months).
The clinical manifestation of AC is nonspecific; therefore, preoperative diagnosis is difficult. However, its manifestations on barium x-ray and contrast computed axial tomography scan are characteristic, and aggregate analysis of the clinic and radiologic data can increase preoperative diagnosis. The main treatment of AC is surgery, and the overall prognosis of these patients is satisfactory.
腹茧症(AC)是一种罕见疾病,其特征为小肠被一层厚厚的纤维膜全部或部分包裹。本文报告了24例病例。我们的目的是探讨腹茧症的诊断和治疗方法。
回顾性分析1997年1月至2007年9月中山大学附属第三医院普通外科收治的24例腹茧症患者的临床表现、诊断、手术治疗及随访结果。
主要临床表现为部分或完全性肠梗阻(87.5%)和腹部肿块(54.2%)。3例术前通过计算机断层扫描确诊,1例通过钡剂X线检查确诊。另外20例通过剖腹探查确诊。所有患者均接受了手术。在所有病例中,我们发现部分或全部小肠被包裹在一层致密、白色、纤维状、茧样的膜中。手术过程中,仔细切除厚膜并松解粘连以解除小肠梗阻。大多数病例术后恢复顺利,在3个月至9年(平均37个月)的随访期内无复发。
腹茧症的临床表现无特异性,因此术前诊断困难。然而,其在钡剂X线和计算机断层扫描造影上的表现具有特征性,综合分析临床和影像学资料可提高术前诊断率。腹茧症的主要治疗方法是手术,这些患者的总体预后良好。