Mete A, Erbasan O, Kemaloglu C, Ozbudak I H, Turkay C
Department of Cardiac and Vascular Surgery, University Hospital of Akdeniz, Antalya, Turkey.
Thorac Cardiovasc Surg. 2009 Mar;57(2):116-8. doi: 10.1055/s-2008-1038726. Epub 2009 Feb 24.
Papillary fibroelastomas (PFEs) are primary cardiac tumors. They are rare benign tumors that occur on the endocardium of the heart, especially on the heart valves. The majority of these benign tumors have been observed on the left side of the heart and involved the aortic and mitral valves; however, occurrence on the right side of the heart has been infrequently reported, with only a few cases documented on the pulmonary valve. Most patients with PFEs are asymptomatic and the tumors are usually found incidentally. The tumors have the potential to cause systemic or pulmonary embolism or obstructive phenomena. We present a rare case of a papillary fibroelastoma occurring on the pulmonary valve with clinical presentation due to pulmonary artery obstruction. The tumor was removed surgically.
乳头状纤维弹性瘤(PFEs)是原发性心脏肿瘤。它们是罕见的良性肿瘤,发生于心脏内膜,尤其是心脏瓣膜。这些良性肿瘤大多见于心脏左侧,累及主动脉瓣和二尖瓣;然而,心脏右侧发生的情况报道较少,仅有少数病例记录在肺动脉瓣。大多数PFEs患者无症状,肿瘤通常是偶然发现的。这些肿瘤有可能导致全身或肺栓塞或阻塞现象。我们报告一例罕见的发生于肺动脉瓣的乳头状纤维弹性瘤,因肺动脉阻塞出现临床表现。该肿瘤通过手术切除。