一名患有急性后部多灶性扁平状色素上皮病变的16岁男性发生急性脑桥梗死。病例报告。

Acute pontine infarct in a 16-year-old man with acute posterior multifocal placoid pigment epitheliopathy. A case report.

作者信息

Jaramillo Arturo, Gaete Germán, Romero Pablo, Orellana Patricia, Illanes Sergio

机构信息

Department of Neurology and Neurosurgery, Clinical Hospital, University of Chile, Santiago, Chile.

出版信息

J Stroke Cerebrovasc Dis. 2009 Mar-Apr;18(2):164-6. doi: 10.1016/j.jstrokecerebrovasdis.2008.08.004.

DOI:10.1016/j.jstrokecerebrovasdis.2008.08.004

PMID:19251194

Abstract

A 16-year-old boy recently diagnosed with acute posterior multifocal placoid pigment epitheliopathy (APMPPE) developed an acute infarct in the left pontine region. No relevant abnormalities were found in the brain and cervical angiography, echocardiography, cerebrospinal fluid, and blood samples. Funduscopically, lesions were multiple circumscribed, creamy yellow patches, flat lesions at the level of the retinal pigment epithelium, and the fluorescence angiography confirmed an APMPPE. All visual and neurological symptoms reverted completely after use of steroid. Our patient is the youngest patient with APMPPE and stroke described so far, being the common age presentation between 20 to 40 years.

摘要

一名16岁男孩近期被诊断为急性后极部多灶性鳞状色素上皮病变（APMPPE），其左侧脑桥区域出现急性梗死。在脑部和颈部血管造影、超声心动图、脑脊液及血液样本检查中未发现相关异常。眼底检查可见病变为多个边界清晰的、乳黄色斑块，是视网膜色素上皮层水平的扁平病变，荧光血管造影证实为APMPPE。使用类固醇药物后，所有视觉和神经症状完全消失。我们的患者是迄今为止所描述的最年轻的APMPPE合并中风患者，该病常见发病年龄在20至40岁之间。